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Oral Surg Oral Med Oral Pathol. Dec;68(6) Familial gigantiform cementoma: classification and presentation of a large pedigree. Young SK(1). Gigantiform cementoma is a rare, benign fibro-cemento-osseous disease of the jaws, seen most frequently in young girls. Radiographically, it typically presents. PDF | Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Undocumented.

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However, the management cementoa the expansive FGCs entails complete surgical removal at an early stage of growth in order to limit the extent of surgery and prevent tooth displacement and loss of residual bone. Undocumented radiographic changes and related bone metabolism disorder are herein hypothesized and discussed. Out of the group of lesions categorized as ODs, only FGC presents clinically with significant jaw expansion.

Abstract The objective of this report is to present an unusual case of a gigantiform cementoma manifesting cemenroma gross gifantiform of the maxilla in a 6-year-old black female. Large vascular malformation in a child presenting with vascular steal phenomenon managed with pial synangiosis. A clinical and radiologic spectrum of cases.

During month follow-up afterwards, the young patient experienced another physical blow of minor-trauma fracture near the femur neck. The objective of this report is to present an unusual case of a gigantiform cementoma manifesting with gross expansion of the maxilla in a 6-year-old black female.

Based on cementoka garnered from CT, it was noteworthy that 2 big circular deficits could be easily detected on both sides of the iliac bones. She is currently under treatment, which she may need to continue until her growth stops in her early 20s.


Familial gigantiform cementoma: classification and presentation of a large pedigree.

Cementoma Search for additional papers on this topic. Distinguishing features of focal cementpma dysplasia and cemento-ossifying fibromas. Articles lacking sources from December All articles lacking sources Infobox medical condition All stub articles. Please review our privacy policy. Support Center Support Center. Clinicopathologic presentation of 3 cases. D Postoperative view of patient after d v.

Gigantiform cementoma – Wikipedia

Author information Article notes Copyright and License information Disclaimer. Before referral, he had experienced 4 times of fractures in bilateral lower extremities within 4 years. F Two bony defects were identified in reconstructed pelvic CT images. A year-old male patient was referred to our hospital for recurrence of a huge benign tumor in oral cavity.

Articles from Medicine are provided here courtesy of Wolters Kluwer Health. Circumstantial evidence and thorough reasoning were presented in his article for differential diagnosis with other easily mistaken diseases, such as Paget disease, cemento-ossifying fibromas and osteogenesis imperfecta. Therefore, we present a case with a large FGC family history so as to sketch a more detailed portrait of such ailment.

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Journal List Dentomaxillofac Radiol v. Dentistry stubs Rare cancers. Therefore, we agree with Noffke et al 14 and Finical 15 in resorting to a complete resection of FGC with curative purposes whenever feasible. Radiographic examination revealed a well-circumscribed lobular radio-opaque mass surrounded by a radiolucent margin. Gigantiform cementoma in a child. Am J Clin Pathol ; Genetically predisposing as FGC seems, emphasis of management has largely been confined to mostly afflicted maxillas and mandibles.

Articles from Dentomaxillofacial Radiology are provided here courtesy of British Institute of Radiology.

From This Paper Figures, tables, and topics from this paper. Plast Reconstr Surg ; Familial gigantiform cementoma FGC is a distinct and uncommon fibro-cemento-osseous lesion with unknown etiology. This page was last edited on 11 Octoberat This article does not cite any sources. Ce,entoma far as our knowledge is concerned, this pathognomonic trait thus necessitates timely and appropriate surgical treatment to prevent these terrible clinical scenarios from spinning out of control.


D Postoperative view of patient after bilateral mandibulectomy. Microscopic examination showed a lobular calcified mass with a peripheral zone of fibropsammomatous tissue corresponding with the radiolucent margin.

Periprosthetic bone mineral density changes after unicondylar knee arthroplasty. RaubenheimerDavid A. E Technetium scintigraphy showed increased tracer uptaker in the chin area. Micrograph demonstrating the bony mass showing a lobular appearance with small marrow spaces arrows. In such scenarios, extensive resection and free-flap reconstruction are required to achieve a better outcome.

Incomplete excision or shave-off contouring is not advised because it may cause a possible aggravation or reactivation of rapid FGC growth. Benign fibro-osseous diseases of the maxillofacial bones. Dentomaxillofac Radiol ; Familial gigantiform cementoma with brittle bone disease, pathologic fractures and osteosarcoma: To sum up, our unusual radiographic and clinical findings of FGC give rise to a renewed understanding and a broad change to the stereotypic definition.

The disorder appears to occur mainly in asymptomatic black females with a mean age of onset of 42 years. C Lateral view of FGC. Familial occurrence of periapical cemental dysplasia. The authors report no conflicts of interest. Loss of lamina dura, decreased skull bone density, and sporadic bony defects all served yigantiform convincing evidence of the serious osseous fragility. You can help Wikipedia by expanding it.